Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular disorder in which a limb may be affected by port wine stains (red-purple birthmarks involving blood vessels), varicose veins, and/or too much bone and soft tissue growth. The limb may be larger, longer, and/or warmer than normal. The cause is unknown.

When should I seek treatment for KTS?

Symptoms and severity of KTS vary for each patient. Symptoms can include bleeding from the affected limb, a skin infection, blood in the urine, or rectal/vaginal bleeding. You could experience pain in the limb, blood clots, anemia and seizures.

Seek treatment to alleviate pain and symptoms as necessary.

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